130959.8

KARTAGENER’S SYNDROME DEXTROCARDIA KARTAGENER’S SYNDROME,DEXTROCARDIA ,BRONCHIECTASIS

62 year old female with situs inversus totalis, dextrocardia, {SLL} heart, inversus of the lungs, left sided liver, right sided stomach and spleen, bronchiectasis, and chronic sinusitis.

aka Primary ciliary dyskinesia (PCD), is a rare, ciliopathic, autosomal recessive genetic disorder

Ashley Davidoff MD